Hydatid cyst is a zoonotic disease caused by CestodaEchinococcus, especially Echinococcus granulosus.Isolated renal hydatidosis is an extremely rare clinical condition associated with nonspecific symptoms and physical findings.Diagnosis can be Drinks Set difficult and depends on imaging findings and histologic examination of excised tissue specimens.Here, we report a case of an isolated right renal hydatid cyst in a 10-year-old girl who presented with progressively worsening right flank pain.Diagnosis was established using multimodal imaging after which she underwent a successful cystectomy, had a smooth post-operative course, and was discharged cutting board with improvement and a continuation of albendazole.